Segmental spinal dysgenesis associated with occult dysraphism: Considerations on management strategies
نویسندگان
چکیده
Segmental spinal dysgenesis is a rare and challenging entity especially when associated with occult dysraphism. Experience with a female patient followed during a period of 10 years spanning from 5 to 15 years of age is reported. During that period the girl underwent three spinal operations consisting in one decompression and spinal cord untethering, one posterior instrumented fusion and a spinal cord re-untethering. Clinical and radiological features are discussed and considerations on optimization of management strategies are made.
منابع مشابه
Occult spinal dysraphism: a challenge in pain management.
Spina bifida is a common birth defect affecting the central nervous system and represents a group of neural tube defects caused by congenital dysraphic malformations of the vertebral column and/or spinal cord. The anatomy in these patients is challenging and includes structural and vascular abnormalities including arteriovenous malformation or fistulae, and fatty substitution of paravertebral t...
متن کاملNewborns with suspected occult spinal dysraphism: a cost-effectiveness analysis of diagnostic strategies.
OBJECTIVE To assess the clinical and economic consequences of different diagnostic strategies in newborns with suspected occult spinal dysraphism. METHODS A decision-analytic model was constructed to project the cost and health outcomes of magnetic resonance imaging (MRI), ultrasound (US), plain radiographs, and no imaging in newborns with suspected occult spinal dysraphism. Morbidity and mor...
متن کاملLipoma and Occult Spinal Dysraphism
Received: 19. 10. 2006. Accepted: 20. 11. 2006. Congenital abnormality, an occult spinal dysraphism �ith spinal lipoma, is a rare dysraphic spinal abnormality. The syndrome, treatments, outcomes, and current controversies are revie�ed. Occult spinal dysraphism usually is usually manifested �ithout clinical changes, either neurological or local changes. Local cutaneous changes associated �ith oc...
متن کاملSkin markers of occult spinal dysraphism in children: a review of 54 cases.
OBJECTIVES To verify the diagnostic value of lumbosacral midline cutaneous lesions in asymptomatic children to detect occult spinal dysraphism (OSD) and to propose a practical approach for clinical investigations with respect to the type of cutaneous lesions observed. DESIGN Retrospective study of 54 children referred to the Department of Pediatric Dermatology between 1990 and 1999 for congen...
متن کاملOccult Spinal Dysraphism in the Presence of Rare Cutaneous Stigma in a Neonate: Importance of Ultrasound and Magnetic Resonance Imaging
Occult spinal dysraphism is defined as a group of dystrophic conditions below an intact cover of dermis and epidermis. Ultrasonography using linear transducers is a fast, inexpensive, and effective method that makes it possible to view the content of the vertebral canal and bone structures. Magnetic resonance imaging (MRI) is reserved for elucidating the type of dysraphism and for planning corr...
متن کامل